UArnold Chiari Malformation: Ulwazi lwaBazali

I-Arnold Chiari malformation:

I-Chiari malformation ithathwa njengemeko yokuba inokuchaphazela abantwana abaninzi naxa bezelwe. Yiyo malformation evela kwinxalenye yengqondo kwaye amaxesha amaninzi iimpawu azicacanga de umntwana afumane indlela yokuqonda isifo kunye nomfanekiso wobuchopho okanye intambo yomqolo ngesizathu esithile.

Unikwe olu hlobo lokufumanisa isifo sijamelene nesifo esinqabileyo, okanye mhlawumbi ngenkqubela phambili entsha kuye kwakho ukubonwa ngokuchanekileyo ngakumbi ngaphandle kokuzimisela ukuyifumana. Oku kungalunganga kukhula njengoko umntwana ekhula. Kwaye ayibonisi kude kube semva kwexesha lobuntwana okanye kwinqanaba lokufikisa.

Yintoni iArnold Chiari Syndrome?

Isifo seArnold Chiari kwenzeka xa izicwili zobuchopho zinwenwela kumjelo womqolo. Ihlala isenzeka kuba icandelo lokakayi lincinci kakhulu kunesiqhelo okanye libunjwe ngendlela engeyiyo kwaye ibangela ukuba ingqondo idandatheke, Oku kuyinyanzela ukuba ikhule iye ezantsi. Ngenxa yoko, kunokubakho into engaqhelekanga ekukhuleni kwengqondo okanye kwikholam yomqolo.

I-Arnold Chiari malformation:

Oogqirha bahlela le mpazamo kwiindidi ezintathu ezahlukeneyo. Ngaba Uhlobo lwe-Chiari malformation uhlobo I qIkhula njengoko ukakayi kunye nengqondo zikhula. Uhlobo lweChiari II kunye nokungalunganga kohlobo III Zikhona xa kuzalwa (zizelwe okanye zizelwe).

Uhlobo lweChiari I iimpawu

Olu hlobo lokungalunganga alubonisi zimpawu, Phantse ayifuni unyango, nangona kwezinye iimeko inokubangela ukuphazamiseka okungafaniyo:

  • iintloko (ngakumbi xa uzisebenzisile njengokukhohlela okanye ukuthimla)
  • Intamo
  • isiyezi
  • ukulungelelaniswa kokungalungelelani kwezandla, ngamanye amaxesha nokuba ndindisholo kunye nokutswina ezandleni nasezinyaweni zombini.
  • iingxaki zombono
  • iingxaki zokuthetha njengokukrala
  • ubunzima bokugwinya, obuhamba nesicaphucaphu, ukukrwitshwa, kunye nokugabha

Unyango olunokwenzeka kuhlobo lweChiari I

I-Arnold Chiari malformation:

Kuba umntwana engahlali eneengxaki ezinzima, ziya kuphela ukujonga rhoqo ii-MRIs ukwenzela ukuba iingxaki ezinokubakho zingakhuli.

Ukuba umntwana unxulunyaniswa neengxaki ezifana nehydrocephalus, sleep apnea, scoliosis okanye syringomyelia, unokunyangwa kolu hlobo lwesifo. Kodwa Unokude udibanise i-posos fossa ukwandisa isithuba Inokuhlala kwi-cerebellum kwaye akufuneki ibeke uxinzelelo kwi-spinal cord.

Uhlobo lwe-Chiari malformation

Olu malformation lwenzeka xa kukho isixa esikhulu sezicubu ezifikelela kumjelo womqolo. Iimpawu kunye neempawu zakho zinokucaca kwizikena ze-ultrasound ezithathwe ngexa lokukhulelwa. Uhlobo lwe-Chiari malformation Ihlala inxulunyaniswa nohlobo lwespina bifida esibizwa ngokuba yi-myelomeningocele, kwaye kukhokelela kwinto yokuba zombini umqolo womqolo kunye nomjelo womqolo awukavali ngaphambi kokuzalwa.


I-Arnold Chiari malformation:

Iimpawu zayo zisusela kwiingxaki zokuphefumla, Ubunzima bokuginya bukhatshwa kukuphinda ubambe, ukuhla kwamehlo okukhawulezayo kunye nobuthathaka obukhulu ezingalweni.

Uhlobo lwe-Chiari malformation uhlobo III

Olu hlobo lolona lubalulekileyo kwimeko. Umva kunye nenxalenye esezantsi yengqondo okanye i-brainstem xa isiya kuvulwa ngokungaqhelekanga ngasemva kokhakhayi. Olu hlobo lwe-III lufunyaniswa ukuba lune-ultrasound xa usana lusesibelekweni sikanina okanye xa luzalwa nje. Amaxabiso okusinda kwabo banengxaki kuwo aphantsi kakhulu kwaye unokuba neengxaki ze-neurological.


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