Iscleroderma ebantwaneni: iimpawu, oonobangela kunye nonyango

ukugula okungaqhelekanga

IScleroderma yi isifo sesikhumba somzimba. Ibonakaliswa ngokuqina okuqhubekayo kwesikhumba. Yi ukugula okungaqhelekanga, Uphuhliso lwayo luyinkimbinkimbi kwaye alukacaci ncam. Ichaphazela phakathi kwama-200 nama-300 abantu kwizigidi zonke.

Siza kukuxelela ukuba yintoni unobangela, iimpawu zabo, unyango olusetyenziswa kakhulu, kwaye ngaphezu kwako konke siya kugxininisa indlela i-scleroderma ebachaphazela ngayo abangaphantsi kweminyaka eli-16 ubudala. Okokuqala, sifuna ukubonisa ukuba kweli nqaku, njengoko uninzi lweengcali lusenza, i-scleroderma kunye ne-systemic sclerosis ziya kusetyenziswa njengamagama afanayo.

Yintoni i-scleroderma okanye i-systemic sclerosis?

izifo zolusu

Sele sihambile ukuba i-scleroderma okanye i-systemic sclerosis sisifo solusu esivela kwimvelaphi yokuzimela, apho kukho ukuqaqamba kwesikhumba okuqhubekayo, nalapho kuchaphazela khona amalungu angaphakathi kunye neempahla. Kukho iseti yezifo, ezinokubonakaliswa oklinikhi okwahlukeneyo okunxulunyaniswa nobungqongqo bolusu, olubizwa ngokuba inkqubo sclerosis.

Akukho datha ngenani ngqo lamakhwenkwe kunye namantombazana analesi sifo, kodwa kuqikelelwa ukuba I-50 yabantwana kwi-100.000 iya kuphuhlisa i-scleroderma yendawo. Le yeyona ndlela ixhaphakileyo yesi sifo kubantwana abangaphantsi kweminyaka eli-10 ubudala, kwaye ichaphazela amantombazana amaninzi. Inkqubo yescleroderma ebantwaneni ingaphantsi kwe-10% yazo zonke iiscleroderma.

Nangona unobangela wescleroderma engaziwa, kuyabonakala ukuba Imfuzo idlala indima ebalulekileyo. Eyona nkolelo yamkelwe ngokubanzi yeyokuba abantwana abachaphazeleka yimfuza, oko kukuthi, abo baneemfuza ezithile, xa bevezwa zizinto ezithile zokusingqongileyo, nokuba ziikhemikhali okanye usulelo, basebenzisa iinkqubo zophendlo lwezifo ekugqibeleni ezikhokelela kwisystemer scleroderma.

Uhlobo lwe-scleroderma oluchaphazela kakhulu abantwana

scleroderma

IScleroderma yahlulwe ngokubanzi yaziifom ezimbini, kuxhomekeke kwinqanaba lokubandakanyeka kwamalungu angaphakathi: i-scleroderma yendawo, kunye ne-systemic sclerosis. Eyokuqala, eyona “ixhaphakileyo ebantwaneni” isikelwe ulusu kwaye kwezinye iimeko iya kuthi ga kwimisipha, amalungu namathambo, anokuchaphazela ukukhula kwamathambo namalungu-

La I-Linear scleroderma, njenge-subtype yendawo, yinto eqhelekileyo kubantwana. Ihlala isebenza iminyaka emibini ukuya kwemihlanu, kodwa ngamanye amaxesha inokuhlala ixesha elide. Ubonakaliswa ngokuqina kwezilonda kulusu kwimigca okanye kwimigca. Ihlala ibonakala esiqwini okanye emilenzeni kwaye ikhawulelwe embindini womzimba. I-scleroderma ehambelanayo ebizwa ngokuba yingozi yokulimala kwe-saber.

La I-Morphea scleroderma yeyona ndlela iqhelekileyo yeklinikhi. Kubantwana babonwa njengeendawo ezinesikhumba esijiyileyo, zihlala zi-oval shape, neziko elimhlophe kunye nemiphetho ye-violet. Ngokuhamba kwexesha ziye zibe mnyama ngakumbi. Ezi zilonda zibonakala rhoqo esiqwini nasemilenzeni. Inikezelwe kwezi ntlobo nakwi-systemic sclerosis ekupheleni kukaJuni, umhla wama-29, usuku lomhlaba lwesi sifo ukuze lwaziwe ngcono.

Unyango kunye neminye imiba

Impilo ebuntwaneni

Isizathu sale nkqubo asaziwa. Kodwa isifo sokuqina kwemithambo asosuleli, okanye lilifaNangona izinto zemfuza zidlala indima, oko akusosifo somhlaza. Kwenzeka nakweyiphi na iminyaka, nangona kunqabile ngokugqithileyo kwabo bangaphantsi kweminyaka eli-10 ubudala.


Nangona ndinako sijongwa “njengesifo esingenabungozi”, sineziphumo ezihle ngobuhle, emva koko iya isiba nzima ngakumbi, ichaphazela amalungu angaphakathi, de ifike kwi-systemic scleroderma, inqabile kakhulu kubantwana nakwishumi elivisayo.

Njengamanyathelo onyango ngokubanzi kuyacetyiswa thintela ukubonakaliswa yingqele, umothuko noxinzelelo. Ngokumalunga namachiza asetyenzisiweyo, kukho iziphumo ezingafaniyo, kufuneka ibe liqela lezonyango elivavanya imeko. Ebusheni, inkxaso yengqondo iyacetyiswa, kwaye ihlala ihlaziywa kwangethuba ukuthintela ikhontrakthi esisigxina. I-Hydrotherapy isetyenziswa ngokubanzi njengonyango, jets zangaphantsi kwamanzi kunye nokuzivocavoca ngokubanzi echibini kwi-36.5 ° C kangangemizuzu eli-15.


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