I-Chiari malformation ibhekwa njengesimo sokuthi kungathinta izingane eziningi noma ngabe zisanda kuzalwa. Kuyinto a ukungalungi okuvela engxenyeni yobuchopho nokuthi izikhathi eziningi izimpawu azicaci kuze kube yilapho ingane iba nenqubo yokuxilonga enomfanekiso wobuchopho bayo noma umgogodla ngesizathu esithile.
Njengoba kunikezwe lolu hlobo lokuxilongwa sibhekene nesifo esingajwayelekile, noma mhlawumbe ngentuthuko entsha kube nokwenzeka ukuxilonga ngokunemba ngaphandle kokuhlose ukukuthola. Lokhu kungalungi kukhula njengoba ingane ikhula. Futhi akubonakali kuze kube sekwephuzile ebusheni noma ebusheni.
Yini i-Arnold Chiari Syndrome?
I-Arnold Chiari Syndrome kwenzeka lapho izicubu zobuchopho zingena emgodini womgogodla. Imvamisa kwenzeka ngoba ingxenye yogebhezi incane kakhulu kunokujwayelekile noma i-misshapen futhi kubangela ukuthi ingqondo icindezeleke, okuyiphoqelela ukuthi ikhule iye phansi. Ngenxa yalokhu, kungahle kube nokungajwayelekile ekukhuleni kobuchopho noma ikholomu lomgogodla.
Odokotela bahlukanisa lokhu kungalungi kube yizinhlobo ezintathu ezihlukene. Ngabe Uhlobo lwe-Chiari malformation I qIkhula njengoba ugebhezi nobuchopho bukhula. Uhlobo lwe-Chiari II kanye nokukhubazeka kohlobo III akhona lapho ezalwa (kungokuzalwa noma ngofuzo).
Izimpawu zohlobo lweChiari I
Lolu hlobo lokungalungi ngokuvamile aluzivezi izimpawu noma izimpawu, Empeleni ayidingi ukwelashwa, yize kwezinye izimo kungadala ukuphazamiseka okuhlukahlukene:
- ikhanda (ikakhulukazi uma uzikhandle njengokukhwehlela noma ukuthimula)
- izinhlungu zentamo
- isiyezi
- ukungahambisani kahle kwesandla, kwesinye isikhathi ngisho nokuba ndikindiki nokushikizana ezandleni nasezinyaweni zombili.
- izinkinga zokubona
- izinkinga zokukhuluma njengokuhaha
- ubunzima bokugwinya, okuhambisana nesicanucanu, ukuklinya nokuhlanza
Ukwelashwa okungenzeka kohlobo lweChiari I
Njengoba ingane ingahlali inezinkinga ezinzima, izophela kuphela ukuhlola ngezikhathi ezithile ngama-MRIs ukuze izinkinga ezingaba khona zingakhuli.
Uma ingane ihlotshaniswa nezinkinga ezifana ne-hydrocephalus, i-apnea yokulala, i-scoliosis noma i-syringomyelia, ingalashwa kulolu hlobo lwesifo. Kepha unganciphisa ngisho ne-posterior fossa ukunweba isikhala Ingangena kwi-cerebellum futhi akudingeki ukuthi icindezele umgogodla.
Uhlobo lwe-Chiari malformation uhlobo II
Lokhu kungalungi kwenzeka lapho kunenani elikhulu lezicubu ezidlulela emgodini womgogodla. Izimpawu nezimpawu zakho zingacaca kusuka kuma-ultrasound scan athathwe ngesikhathi ukhulelwe. Uhlobo lwe-Chiari malformation uhlobo II Imvamisa kuhlotshaniswa nesimo se-spina bifida esibizwa nge-myelomeningocele, futhi kuholela eqinisweni lokuthi womabili umgogodla nomgogodla womgogodla awuzange uvalwe ngaphambi kokuzalwa.
Izimpawu zayo zisukela ezinkingeni zokuphefumula, Kunzima ukugwinya okuhambisana nokuphinda kutholakale, ukunyakaza kwamehlo okusheshayo okuphansi kanye nobuthakathaka obukhulu ezandleni.
Uhlobo lwe-Chiari malformation uhlobo III
Lolu hlobo yisimo esibi kakhulu kulesi simo. Ingxenye engemuva nengaphansi yobuchopho noma i-brainstem lapho ifinyelela ekuvulekeni okungavamile ngemuva kogebhezi. Lolu hlobo lwe-III lutholakala lune-ultrasound lapho ingane ingaphakathi kwesizalo sikamama noma lapho izalwa nje. Izinga lokusinda kulabo abaphethwe yilo liphansi kakhulu futhi ungaba nezinkinga zemizwa.